Ductal paucity and Warkany syndrome in a patient with congenital extrahepatic portocaval shunt
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منابع مشابه
A Case of Pulmonary Arterial Hypertension Associated with Congenital Extrahepatic Portocaval Shunt
Congenital extrahepatic portocaval shunt (CEPS) is a rare anomaly of the mesenteric vasculature in which the intestinal and splenic venous drainage bypasses the liver and drains directly into the inferior vena cava, the left hepatic vein or the left renal vein. This uncommon disease is frequently associated with other malformations and mainly affects females. Here we report a case of pulmonary ...
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A 7-year-old boy presented with recurrent cholangitis, failure to thrive, and progressive splenomegaly. On examination, he had severe pallor, clubbing, and splenohepatomegaly. Lab results showed anemia (hemoglobin 7.2 g/dL) and normal liver functions. Abdominal ultrasound showed hepatosplenomegaly with coarsened liver echotexture and multifocal intrahepatic biliary radical (IHBR) dilatation. Th...
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History: A 3.5-months-old male presented to us with small bowel type of diarrhea and recurrent non-bilious vomiting since birth; jaundice since 2.5 months of age; swelling all over body, clay colored stools, fever, cough and respiratory difficulty since 3 months of age, and refusal to feed from 2 days prior to admission. He also had prolonged bleeding at the site of intramuscular injection. The...
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ژورنال
عنوان ژورنال: World Journal of Hepatology
سال: 2014
ISSN: 1948-5182
DOI: 10.4254/wjh.v6.i5.358